Antisense RNA for treating cancer and inhibition of metastasis and vectors for antisense sequestration

09702880 ยท 2017-07-11

Assignee

Inventors

Cpc classification

International classification

Abstract

Provided is the use of antisense RNA and methods for the treatment, diagnosis and prophylaxis of cancer comprising administering said antisense RNA, particularly miRs 15 and 16 to a patient in need thereof.

Claims

1. A method of diagnosing progression of a cancerous prostate tissue or tumor to an advanced stage of cancer, said method comprising: detecting levels of expression of miR 15a and miR 16-1 in one or more cells from the cancerous prostate tissue or cancerous prostate tumor, wherein miR 15a has the sequence set forth in SEQ ID NO:4 and miR 16-1 has the sequence set forth in SEQ ID NO:5, and wherein the detecting step comprises performing Northern hybridization or in situ hybridization, using at least one miR 15a specific probe comprising sequence specific for SEQ ID NO:4 and at least one miR 16-1 specific probe comprising sequence specific for SEQ ID NO:5; whereby progression of prostate cancer to an advanced stage is diagnosed when detected levels of miR 15a and miR 16-1 are down-regulated in the cells from the cancerous prostate tissue or cancerous prostate tumor as compared to normal prostate cells, primary prostate tumor cells or benign prostate tissue; and wherein the at least one miR 15a specific probe and the at least one miR16-1 specific probe are each 100% specific for the seed sequence AGCAGCA.

2. A method of diagnosing progression of a cancerous prostate tissue or prostate tumor to an advanced stage and treating cancerous prostate tissue or prostate tumor, said method comprising the steps of: (a) detecting levels of expression of miR 15 and miR 16 in one or more cells from the cancerous prostate tissue or prostate tumor, whereby an advanced stage of prostate cancer is diagnosed when miR 15 and miR 16 are down-regulated in cancerous prostate tumor cells or tissue as compared to normal cells, primary tumor cells or tissue or benign prostate tissue; wherein the miR 15 is miR 15a and wherein the miR 16 is miR 16-1; wherein the detecting step comprises: (i) performing quantitative real-time polymerase chain reaction, using at least one miR 15a specific primer comprising sequence specific for SEQ ID NO:4 and at least one miR 16-1 specific primer comprising sequence specific for SEQ ID NO:5; or (ii) performing Northern hybridization or in situ hybridization, using at least one miR 15a specific probe comprising sequence specific for SEQ ID NO:4 and at least one miR 16-1 specific probe comprising sequence specific for SEQ ID NO:5; and (b) administering antisense RNA to a patient in need thereof or causing antisense RNA to be expressed in a patient in need thereof, wherein the antisense RNA is miR 15 and miR 16-1, or is complementary to all or part of the 3 untranslated region (UTR) of Cyclin D1, Wnt3a, and/or bFGF protein mRNA; thereby diagnosing an advanced stage of the prostate cancer and treating the cancerous prostate tissue or prostate tumor.

3. The method of claim 2, wherein the antisense RNA has the sequence of SEQ ID NO: 4 and SEQ ID NO:5.

Description

BRIEF DESCRIPTION OF THE FIGURES

(1) FIGS. 1A-C. miR-15a and miR-16 are frequently downregulated in prostate tumors.

(2) FIG. 1A miR-15a and miR-16 expression was analyzed by real time PCR in primary cells isolated by cancer prostate samples from 20 patients diagnosed with prostatic adenocarcinomas. miR levels were evaluated as relative expression over those of cells from normal prostate tissues (dotted line). Real time PCR data are mean values of four independent experiments performed in duplicated. FIG. 1B In situ hybridization analysis of miR-15a and miR-16 expression in normal and tumor prostatic tissues (magnification 40). FIG. 1C Hematoxylin-Eosin staining (left) and detection of miR-15a and miR-16 by in situ hybridization (central and right) in serial sections from prostatic adenocarcinoma. Tumor (red arrows) and non-neoplastic prostate epithelial cell areas (black arrows) are indicated.

(3) FIGS. 2A-F. Targeting of miR-15a and miR-16 promotes prostate cell proliferation and invasiveness.

(4) FIG. 2A Schematic description of the functional elements in the TW3UTRdecoy15/16 vector. CMV: cytomegalovirus immediate early promoter; PGK: phosphoglycerate kinase gene promoter, PURO: puromycin resistance gene. FIG. 2B Real time PCR evaluation of miR-15a and miR-16 levels in RWPE-1decoy15/16, LNCaP and primary tumor with normal miR expression, transduced with control (TW3) or decoy15/16 vectors. The untrasformed prostate cell line RWPE-1 was used as reference. FIG. 2C Cell growth of RWPE-1 and primary tumor cells with normal miR expression, transduced with decoy15/16 or with the empty vector (TW3). FIG. 2D Cell cycle analysis by cytofluorimetric profiling of BrdU/7AAD-stained RWPE-1 cells transduced with TW3 or decoy15/16 vector. Results were analyzed by two-way ANOVA and Bonferroni post-tests. P value for the two groups was <0.001. FIG. 2E Representative soft-agar colony formation assay for RWPE-1 TW3 and RWPE-1decoy15/16 cells. Data are means.d. of three independent experiments. FIG. 2F Migration assay for RWPE-1 TW3 and decoy15/16 cells maintained in standard culture medium (Control) or in prostate cancer fibroblast-conditioned medium (Conditioned). Data were analyzed by t-test. (**) represents a P value <0.01 and (***) represents a P value <0.001. Data are means.d. of four independent experiments.

(5) FIGS. 3A-G. Restoration of miR-15a and miR-16 induces growth arrest and apoptosis in defective prostate cancer cells.

(6) FIG. 3A Schematic description of TWmiR-15/miR-16. The miR-15a/miR-16-1 cluster was subcloned in the TWEEN vector under the control of the CMV promoter. FIG. 3B Real time PCR evaluation of miR-15a and miR-16 expression in LNCaP cells transduced with TWmiR-15a/miR-16 vector. Transduced cells were compared with cells infected with empty vector (TW) and with RWPE-1 cell line. FIG. 3C Cell growth of LNCaP cells infected with empty vector (TW) or TWmiR-15/miR-16. Data are means.d. of four independent experiments. FIG. 3D Cell death of normal (RWPE-1) and tumor (LNCaP) cells transduced with TWmiR-15a/miR-16 or control vector (TW) was evaluated 48 hours after lentiviral infection. FIG. 3E Flow cytometry profiles of LNCaP and RWPE-1 cells infected with TW and TWmiR-15a/miR-16 viruses. GFP expression is shown 24 h (Day 0) and 11 days (Day 10) postinfection. FIG. 3F Real time PCR analysis of miR-15a/miR-16 expression on miR-defective prostate tumor primary cells after transduction with TWmiR-15a/miR-16 or empty TW vector. Primary normal prostate cells were used as reference. FIG. 3G Cell death evaluation in tumor and normal prostate primary cells infected as in f. Data are means.d. of three independent experiments.

(7) FIGS. 4A-F. miR-15a and miR-16 target Cyclin D1 and Wnt3a.

(8) FIG. 4A pGL3 and pGL3-UTRs vectors were cotransfected with miR-15a, miR-16 or miR scrambled oligos. Luciferase activity was detected 48 hours posttransfection. Data are means.d. of five independent experiments. FIG. 4B Western blotting analysis of miR-15a/miR-16 targets in RWPE-1, RWPE-2, LNCaP and miR defective tumoral primary cells (Tumor) transduced with either decoy15/16 or TWmiR-15a/miR-16 and the corresponding control vectors. FIG. 4C Wild type (grey and blue) and decoy15/16 RWPE-1 (yellow and light blue) cells were transfected with sense oligos specific for both miR-15 and 16 (miR15-16); wild type RWPE-1 cells were also treated with antisense oligos for miR-15 and 16 (-miR15-16). The reported values were obtained using their respective scramble treated control cells as reference. Data are means.d. of three independent experiments. FIG. 4D Bcl-2 and cyclin D1 immunohistochemical staining of normal prostate tissues and miR-15/16 defective tumors. One representative case of three non-tumoral controls and five miR-15/miR-16 defective tumors is shown. FIG. 4E Inverse correlation between miR-15/16 and target proteins in primary prostate cultures. The miR expression was evaluated by real time PCR, normalizing over a normal sample (N1) used as reference. Protein levels were reported as Western blotting densitometry normalized over -actin protein expression and then compared to N1. Nine indicative samples are shown. Spearman correlation analysis was performed between miR and targets levels. A correlation coefficient of 0.81 with a p=0.008 indicates an inverse relationship between miR-15/16 expression and the levels of cyclin D1, Bcl-2 and Wnt3a. FIG. 4F Western blot analysis of -catenin, pAKT, pGSK3 , pERK, pRb in LNCaP and RWPE-1 cells. One representative of three independent experiments is shown.

(9) FIGS. 5A-D. Effects of miR-15a/miR-16 knockdown on tumor development in vivo.

(10) FIG. 5A Tumorigenic potential of 410.sup.6 (triangles) or 10.sup.7 (circles) untransformed RWPE-1 cells transduced with decoy15/16 or control TW3 vector. Data are means.d. of five mice analyzed per each group in three independent experiments. FIG. 5B Tumor size after injection of 410.sup.6 tumorigenic RWPE-2 cells transduced with TW3 or decoy15/16 vectors. Data are means.d. of five mice analyzed per each group in two independent experiments. FIG. 5C 2.810.sup.6 wild type RWPE-1 cells together with 1.210.sup.6 RWPE-1 decoy15/16 cells were resuspended in matrigel and injected subcutaneously in NOD-SCID mice. After 12 weeks, mice were sacrificed and tumor sections were stained with anti-GFP antibody. Arrows indicate GFP+ cells at the tumor front. Six mice were analyzed in two independent experiments. FIG. 5D Hematoxylin-eosin staining of mouse prostates treated with antagomir by local injection of either antagomir-15a in combination with antagomir-16 (Antagomir-15/16) or antagomir-1 as a control. Five mice per each group were analyzed in two independent experiments.

(11) FIGS. 6A-C. Therapeutic effect of viral miR-15a/miR-16 delivery on subcutaneous NOD-SCID mouse xenografts.

(12) FIG. 6A Effect on tumor growth of miR-15a/miR-16 reconstitution. Tumors generated four weeks after injection of 810.sup.6 LNCaP cells were treated with virus particles containing TW and TWmiR-15a/miR-16 vectors. Data are means.d. of three independent experiments with three mice per each group. FIG. 6B Immunohistochemical analysis of LNCaP xenografts following injection of TW viral particles as in FIG. 6A. Sections were stained with control or anti-GFP antibodies two weeks after virus treatment. A larger area at low magnification is shown at the bottom. FIG. 6C Hematoxylin-eosin staining (magnification 10) of six weeks LNCaP xenografts, two weeks after injection of TW and TWmiR-15a/miR-16 viral particles. Rare living tumor cell islands in a necrotic tumor treated with TWmiR-15/16 vector are indicated by arrows.

(13) FIGS. 7A-B. Characterization of Primary prostate cells

(14) Expression of Thy-1, Cytokeratin 18/8, AMACR and p63 in tumoral FIG. 7A and normal FIG. 7B prostate primary cells from freshly-isolated surgical prostate specimens as determined by immunocytochemistry on cytospin centrifuged cells and flow cytometry.

(15) FIG. 8. In situ hybridization for miR-15a and miR-16

(16) miR-15a and miR-16 expression by in situ hybridization in tissue sections, 10 magnification. Both images contain tumoral (red arrows) and non-tumoral (black arrows) tissue.

(17) FIGS. 9A-B. Validation of decoy15/16 vector

(18) FIG. 9A Percentage of GFP positivity and relative mean fluorescence of 293T cells transfected with decoy15/16 vector in the presence of scrambled, miR-16 or miR-15a oligos. FIG. 9B Northern blotting analysis of 293T cells cotrasfected with increased ratios of decoy15/16 vector versus expression vector TWmiR-15a/miR-16. The total amount of plasmid DNA was maintained at 20 using empty vector TW3. Band relative quantification for miR-15a and miR-16 northern blotting is reported.

(19) FIGS. 10A-B. Decoy15/16 infected RWPE-1 cells showed a significant decrease of both miR-15a and miR-16

(20) FIG. 10A Flow cytometry analysis of GFP expression in RWPE-1 cells infected with TW3 and decoy15/16 vectors. Mean fluorescence intensity of GFP expression was evaluated comparing RWPE-1 wild type cells to TW3 and decoy15/16 cells. FIG. 10B RWPE-1 cells infected with TW3 and decoy15/16 vectors were analyzed for endogenous miR expression by Northern blotting.

(21) FIGS. 11A-B. No correlation between Rb expression and loss of miR-15/16 in prostate cancer cells

(22) FIG. 11A Western blotting analysis of Rb expression in miR-15/miR-16 defective LNCaP and in RWPE-1 cells. FIG. 11B Rb expression profile in primary prostate tumor cells (T1-T8) as compared to miR-15/miR-16 level, non-tumoral primary cells (N) were used as control reference.

(23) FIGS. 12A-D. Effect of miR-15a/miR-16 modulation on the cytotoxic activity of docetaxel

(24) FIG. 12A Evaluation of cell death and caspase activation in RWPE-1 cells infected with TW3 or decoy15/16 vectors and treated with 10 ng/ml of docetaxel. Caspase activation was measured after 4 h of treatment. FIG. 12B Evaluation of cell death and caspase activation in LNCaP cells infected with TW or TWmiR-15a/miR-16 vectors and exposed to 10 ng/ml of docetaxel. FIG. 12C-D Evaluation of cell death and caspase activation in miR15a/miR-16 defective or non-defective (normal) primary tumor cells transduced as indicated and treated with 10 ng/ml docetaxel. FIG. 12C. Cell death was measured after 24 h exposure to docetaxel. FIG. 12D. Caspase activation in LNCaP and primary tumor cells was measured after 18 h of treatment. Data are means.d. of at least three independent experiments for each group.

(25) FIGS. 13A-C. Binding site evaluation for miR-15a and miR-16

(26) FIG. 13A pGL3 and pGL3-3UTRs vectors were cotransfected with miR scrambled, miR-15a, miR-16 or with a mixture of miR-15a and miR-16 oligos. Luciferase activity was detected at day 2 posttransfection. FIG. 13B Sequences and introduced mutations of the miR-15a and miR-16 binding sites. Sequences of mir-15 and mir-16 are given in SEQ ID NOs:4 and 5, respectively, and the remaining sequences are given in SEQ ID NOs:26-33, sequentially. FIG. 13C Luciferase assay was performed using pGL3-UTRs bearing mutations in the putative miR target sites.

(27) FIGS. 14A-D. Relative protein quantification of Western blotting analysis

(28) FIG. 14A-C Relative protein quantification of miR-15a/miR-16 targets in RWPE-1 and RWPE-2 cells FIG. 14A, LNCaP cells FIG. 14B or miR defective primary tumoral cells transduced as indicated FIG. 14C. FIG. 14D Relative protein quantification of -catenin, pAKT, pGSK3 , pERK, pRb. Values are obtained by normalizing each sample with the corresponding expression of -tubulin as compared with the level measured in LNCaP cells. Data are means.d. of three independent experiments.

(29) FIGS. 15A-C. Cyclin D1, Wnt3a and Bcl-2 gene transfer into RWPE-1 cells

(30) FIG. 15A Cell growth of RWPE-1 cells transduced with cyclin D1, Wnt3a and Bcl-2 genes. Control value was obtained by the combined mean number of TW3 and TW transduced cells. Histogram bars represent the cell number obtained after 4 days of culture. All samples were 20,000 cells at day 0. FIG. 15B Cell cycle analysis as measured by cytofluorimetric profiling of BrdU/7AAD-stained RWPE-1 cells transduced with decoy15/16, cyclin D1, Wnt3a or Bcl-2. Values were reported as fold increase over empty vector transduced cells (TW3 and TW vectors). Data are means.d. of three independent experiments. FIG. 15C Migration assay for RWPE-1 TW3, decoy15/16, cyclin D1, Wnt3a and Bcl-2 cells maintained in standard culture medium (Control) or in prostate cancer fibroblast-conditioned medium (Conditioned). Data are means.d. of four independent experiments.

(31) FIGS. 16A-B. Effect of Bcl-2, Cyclin D1, Wnt3a gene modulation on the cytotoxic activity of docetaxel

(32) FIG. 16A Western blotting analysis of RWPE-1 transduced with Bcl-2, cyclin D1, Wnt3a and empty vector (TW), alone or in double combination. FIG. 16B Evaluation of cell death in RWPE-1 cells transduced as indicated and treated for 12 h with 10 ng/ml docetaxel. Control is the mean death value of TW3, TW and TW/TW transduced cells. Data are means.d. of three independent experiments.

(33) FIGS. 17A-G: BTG-2 derepression impairs tumor cell growth.

(34) FIG. 17A Schematic description of the functional elements in the TW3UTR BTG-2 vector. CMV: cytomegalovirus immediate early promoter; PGK: phosphoglycerate kinase gene promoter, PURO: puromycin resistance gene. FIG. 17B Flow cytometry profiles of RWPE-2 cells infected with TW3 and TW3UTR BTG-2 viruses. BTG-2 expression is shown 48 h postinfection. FIG. 17C RWPE-2 cells transduced with TW3UTR BTG-2 impairs cell growth over TW3 infected population. After day 3 the TW3UTR BTG-2 transduced cells undergo a massive conuterselection. FIG. 17D Cell cycle analysis by cytofluorimetric profiling of BrdU/7AAD-stained RWPE-2 cells transduced with TW3 or TW3UTR BTG-2 vector. One representative experiment was reported. FIG. 17E-F Western blot analysis (FIG. 17E) and graph (FIG. 17F) of Cyclin D1, pRb, PTEN, p63 and sprouty in RWPE-2 cells. RWPE-1 cells were used as normal control cell line. One representative of three independent experiments is shown. FIG. 17G Cell growth of PC-3 cells transduced with BTG-2 gene. Histogram bars represent the cell number obtained after 5 days of culture. After day 5 the BTG-2 transduced cells undergo a massive counterselection.

(35) FIGS. 18A-D: Control experiments.

(36) FIG. 18A BTG-2 flow cytometry profile of 22Rv1 cells transduced with TW3UTR BTG-2. C-12 antibody was used. FIG. 18B Western blotting on 293T cell transduced with BTG-2 gene. S-20 antibody was used. FIG. 18C Immunoprecipitazion of BTG-2 protein in PC-3 TW-BTG-2 transduced cells. BTG-2 protein was immunoprecipitated with C-12 antibody and detected for western blotting with antibody used in Passeri D. Mol Cell Biol. 2006 July. FIG. 18D Flow cytometry analysis (FACS) of PC-3 transduced with TW and TWBTG-2 vectors.

(37) FIG. 19: In vivo BTG-2 derepression impairs tumor mass proliferation.

(38) Effect on tumor growth of miR-21 sequestration. Tumors generated four weeks after injection of 8106 RWPE-2 cells were treated with virus particles containing TW3 and TW3UTR BTG-2. vectors. Data are means.d. of three independent experiments with three mice per each group.

EXAMPLE 1

(39) Methods

(40) Cells.

(41) LNCaP, RWPE-1 and RWPE-2 cell lines were obtained from ATCC and cultivated in the recommended medium. Tissue dissociation and isolation of primary prostate cells were performed as described [41] with some modifications (see Supplementary Methods). Tumoral and non-tumoral prostate surgical specimens were cultured in collagen-coated plate with BRFF-HPC1 medium (AthenaES, Baltimore Md.). The purity of human prostate primary cell preparation was confirmed by immunocytochemistry and FACS analysis through the expression of the stromal marker Thy-1 and cytokeratins (>85%). Tissues were obtained from radical prostatectomy at the Department of Urology, S. Giovanni Bosco Hospital of Turin, Italy. All samples were collected with informed consent of the patients.

(42) Immunohistochemistry and In Situ Hybridization.

(43) Immunohistochemistry experiments were performed on 2 m thick formalin-fixed paraffin-embedded tissue sections. After dewaxing, sections were permeabilized for 30 min with TBS containing 0.4% Triton X-100 and blocked for 30 min with TBS containing 5% BSA. Then, sections were incubated overnight at 4 C. with the primary antibodies. Mouse anti-Bcl-2 (1:100) was from BioGenex (San Ramon, Calif.); mouse anti-cyclin D1 (1:20) from Dako Corp. (Carpintera, Calif.); rabbit anti-EGFP (1:200) from Invitrogen (Carlsbad, Calif.). After washing with TBS, sections were incubated for 1 hr at RT with the biotinylated anti-mouse or anti-rabbit secondary antibody (1:500, Jackson Lab, Maine) and treated with streptavidin conjugated with HRP (DAKO Corp., Carpintera, Calif.). Finally, the signal was detected using diaminobenzidine (DAB) as chromogen. Sections were counterstained with hematoxylin, dehydrated and mounted with xylene.

(44) LNA-modified probes biotinylated at 5-end (Exiqon), were used to detect the in situ hybridization signal for miR-15a and miR-16 on formalin-fixed paraffin-embedded prostate tissue. In situ hybridization was performed as described by Nelson and colleagues[42] with some modifications (see Supplementary Methods).

(45) Western and Northern Blotting.

(46) Protein extracts were prepared by resuspending cell pellets in 1% NP40 lysis buffer (20 mM Tris/HCl pH 7.2, 200 mM NaCl, 1% NP40) with Protease and Phosphatase Inhibitor Cocktails I and II (Sigma-Aldrich). Equal amounts of proteins were used for SDS-PAGE. Samples were analyzed by standard immunoblot procedure with anti-Bcl-2, anti--catenin, anti-pAKT (Ser-473), anti-pGSK3 (Ser9), anti-pRb (Ser807-811) (Cell Signalling Technology, Danvers, Mass.), anti-cyclin D1, anti-Wnt3a, anti-pERK, and anti-Rb (Santa Cruz) antibodies. Anti--actin (Oncogene Research Products, San Diego, Calif.) or anti--tubulin (Sigma) monoclonal antibodies were used as loading control. Northern blotting was performed with antisense probe for mature miRs as reported [20].

(47) Soft-Agar Colony and Motility Assay.

(48) For the soft-agar assay, TW3 and decoy15/16 RWPE-1 cells were resuspended in culture medium supplemented with 0.4% agar and plated at a density of 100, 250, 500 cells/well in duplicate in a 24-well plate, previously coated with a 3-mm layer of the same modified medium. Cells were cultured for two weeks and then photographed. Three separated experiments were performed for each cellular density. Chemotaxis was tested in modified Boyden chambers containing porous (8-m), uncoated polycarbonate membranes (Corning Incorporated, Nagon Park Acton, Mass.), as described in Supplementary Methods.

(49) Generation of Lentiviral Vectors and Gene Transfer.

(50) For TWmiR-15a/miR-16 generation, miR-15a/miR-16-1 precursor DNA was PCR-amplified from human genomic DNA. The amplified fragment spanning 724 bp (NCBI36: ch13:49519256:49523338) was subcloned into the lentiviral vector TWEEN [20] under the CMV promoter. miR transgene expression was assayed by real time PCR using the appropriate oligonucleotides from Applied Biosystems.

(51) The TW3UTR vector was obtained by modifying the EGFP 3UTR of the TWEEN vector through the insertion of a multicloning site (XhoI-XbaI) that allowed the subcloning of antisense miR sequences. Then the EGFP modified 3UTR cassette was inserted under the CMV promoter control. Moreover, a puromycin resistance gene was inserted under the PGK promoter control to allow the selection of transduced cells.

(52) For decoy-15/16 vector generation, tandem sequences complementary to miR-15a separated by a 18 bp unrelated spacer were synthesized as oligonucleotides (Invitrogen) and then inserted into XhoI-XbaI multicloning site in TW3UTR vector. Given the high homology between miR-15a and miR-16 especially in their seed sequence (residues 2-8), decoy sequences can match to miR-16 (FIGS. 9A-B and FIGS. 10A-B). This design, using multiple copies of complementary targets, was intended to optimize repression of the transgene in the presence of the miRNAs [5]. The sequestering capacity of the decoy vector was further validated by Northern blotting analysis of miR-15a and miR-16 in 293T cells co-transfected with TWmiRNA15/16 and decreasing concentrations of Decoy15/16 vector (1:3, 1:2, 1:1). To maintain an equal total amount (20 g) of plasmid transfection in all conditions, we added variable doses of TW3 vector to replace or complement the Decoy15/16. The TW vector (20 g) and a combination of TWmiR15/16 (5 g) and TW3 (15 g) vectors were used as negative and positive controls, respectively (FIG. 9B).

(53) Recombinant lentiviral particles were obtained as described [43]. Cells were infected with 110.sup.6 TU particles of viruses, as previously indicated [43]. For in vivo experiments, the viral supernatant was concentrated 250-fold. To obtain high-titre vector stocks, virus was ultracentrifuged [43] and injected in 200 l of PBS directly into tumor xenografts of NOD-SCID mice. Bcl-2, cyclin D1 and Wnt3a genes were subcloned into the TWEEN vector. Double exogenous expression of Bcl2/cyclin D1 and Bcl-2/Wnt3a was obtained by infecting with Bcl-2 virus particles the RWPE-1 cells stably transduced with either cyclin D1 or Wnt3a. Selection of double infected cells was obtained by flow cytometry sorting with FACSaria (Becton Dickinson), setting the sorting gate on cells brighter then those with single infection. The same procedure was followed for obtaining empty vector control cells.

(54) Reporter Assays.

(55) 3UTR segments of Bcl-2, cyclin D1 and Wnt3a were amplified by PCR from normal human genomic DNA and subcloned into the 3UTR of the firefly luciferase coding sequence into pGL3-Promoter (Promega), see Supplementary Methods. Then K562 (510.sup.4 cells per well) were transfected using Lipofectamine 2000 (Invitrogen) following the manufacturer's instructions. The transfection mix included: (a) 0.8 g of pGL3-3UTR plasmid and 50 ng of the control vector pRL-TK (Promega); (b) 25 pmol of either non-targeting RNA control (scrambled) or miR-15a or miR-16 oligonucleotides (Ambion). Forty-eight hours post-transfection, firefly and renilla luciferase activities were measured using the Dual Luciferase Assay kit (Promega). Transfection efficiencies were normalized by calculating the ratio of firefly to renilla. For each construct the relative luciferase activities were calculated by dividing the values obtained in the transfection of miR-15a and miR-16 by those of miR scrambled. Each experiment was performed in duplicate and replicated five times.

(56) Target Screening.

(57) In this study, we used three publicly available search engines for target prediction: TargetScan (Release 2.1), http://genes.mit.edu/targetscan [4, 44, 45]; miRanda, http://www.microrna.org [46]; and PicTar, http://pictar.bio.nyu.edu [47]. The putative targets common to the different algorithms were obtained by sequentially inputting TargetScan hits to PicTar and finally to miRanda. The p-value for any target in this list was computed by TargetScan and a threshold value of <0.1 was then set for positive selection. This procedure yielded a list of 61 top-scoring candidates of which only a few could directly promote cell proliferation.

(58) RNA Extraction and Quantitative Real Time PCR.

(59) Total RNA was extracted with acid phenol methods. Fifty nanograms of RNA were reverse transcribed with M-MLV reverse transcriptase (Invitrogen) and cDNA was diluted 1:10 in the PCR reactions. Housekeeping gene reverse transcription was performed using random primers, while miR specific looped-primers were used for miR-15a and miR-16 reactions. TaqMan microRNA assays (Applied Biosystems) for miR-15a and miR-16 were used for PCR amplification. Normalization was performed using snRNA U6 and rRNA S18 as references (RNU6B TaqMan microRNA assay and S18 TaqMan assay on demand, Applied Biosystems). Since we obtained comparable results with both housekeeping genes, we performed all experiments using S18 as a reference. Calibration was performed using cDNA samples from normal prostate primary cells or the RWPE-1 cell line. Values are expressed in terms of 2.sup.CT where C.sub.T=C.sub.TsampleC.sub.Tcalibrator, C.sub.T was the difference in threshold cycles between the miR and S18 amplicons, and C.sub.T was a parameter given by ABI PRISM 7700 Sequence Detector software by negative correlation with an internal reference dye (ROX).

(60) Cytofluorimetric and Viability Assays.

(61) For cell cycle determination, 2.510.sup.5 RWPE-1TW3 and RWPE-1decoy15/16 cells were analyzed with the BD Pharmingen BrdU Flow Kit staining protocol. Cells were seeded in 6 wells plate for 24 h. Then BrdU was added in culture medium and maintained for 1 h at 37 C. in incubator. Fixation and permeabilization of the cells was performed with BD Cytofix/Cytoperm Buffer following the protocol indication. Cells were stained with anti-BrdU-APC for 20 minutes at room temperature and treated with 7-AAD before FACS analysis. BrdU-unlabelled cells from the same population were used as negative control. Cells were analyzed with LSR II (BD). Cell death was evaluated by trypan blue staining, PI staining and flow cytometry analysis, Apo-percentage assay (Biocolor) and Cell Titer kit (Promega). Caspase activation was detected using APO-one Homogeneous Caspase3/7 Assay Kit (Promega).

(62) Statistical Analysis.

(63) Data are presented as the means.d. Results of BrdU assays were analyzed by two-way ANOVA and Bonferroni post-tests. Migration assay was analyzed with Student's t-test. Spearman correlation analysis was performed between miR and corresponding targets levels.

Supplementary Methods

(64) Primary Cells Isolation and Characterization

(65) Benign and neoplastic tissue specimens were taken from the prostate base in the transition zone and the suspicious areas in the peripheral zone, respectively. The tumoral and non-tumoral nature of each sample was confirmed by histopathological examination. Freshly-isolated surgical tumor specimens were collected and treated with collagenase for enzymatic dissociation. The homogenate suspension was maintained in culture in collagen-coated plate with a specific medium that allowed the propagation of primary prostate cells (BRFF-HPC1 medium, AthenaES, Baltimore, Md.). In this condition, cells grew in monolayer assuming a round-shape aspect visible under the microscope.

(66) To determine the number of luminal cells and those contaminating fibroblasts, cells were stained for cytokeratin 18 (Clone5D3 by NovoCastra, used 1:10) and Thy-1 (Clone 5E10 by Becton Dickinson, used 1:50), respectively. The percentage of tumor cells was evaluated with anti-AMACR (1:50, Sanova Pharma, Vienna, Austria), while normal basal cells were detected with anti-p63 (1:50, BioGenex). For flow cytometry, Thy-1 staining was performed in PBS at 4 C. for 1 h, while the other antibodies were used after fixation and permeabilization with parafolmaldehyde 2% and Triton 0.1%. For immunocytochemistry on cytospin preparation, cells were fixed for 10 min with 4% paraformaldehyde, abundantly rinsed in PBS and permeabilized for 5 min with 0.2% Triton X-100. Nonspecific binding was blocked by treatment with 1% BSA for 1 hour and, finally, cells were incubated at RT for 1 hour with primary antibodies. After washing, cells were incubated for 1 hr with the biotinylated secondary antibodies (1:500, Jackson Lab) and treated with streptavidin-HRP (DAKO Corp.). The signal was detected using diaminobenzidine (DAB) as chromogen.

(67) Cells were counterstained with hematoxylin, dehydrated and mounted with xylene. Only cultures with >85% enrichment of prostatic epithelial cells were used for further experiments. To reduce the fibroblast contamination, we treated the cell culture plate with a diluted (1 g/L) trypsin solution for 1-2 minutes once or twice. Prostate epithelial cells are more resistant to this treatment because they rapidly grow in round compact areas, while contaminating fibroblasts are still isolated and detach more easily from the culture dish.

(68) Conditioned Medium and Motility Assay.

(69) Two10.sup.4 RWPE-1 TW3 and decoy15/16 cells were suspended in 200 l of PRF-SFM (Phenol Red Free-Serum Free Medium, Invitrogen) and plated into upper wells. Lower wells contained 500 l of cell culture medium (Supplemented Keratinocyte medium) or PRF-SFM-Conditioned Medium (PRF-SFM-CM), prepared by growing human prostate cancer fibroblasts in PRF-SFM for 48 h; conditioned medium was collected, filtered and kept in 20 C. until use.

(70) To study chemotaxis, Supplemented Keratinocyte medium and PRF-SFM-CM were added to lower wells only. After 72 h, the cells in the upper wells were removed, whereas the cells that migrated to the lower wells were fixed and stained in Coomassie Blue solution (0.25 g of Coomassie blue: 45 ml water: 45 ml methanol: 10 ml glacial acetic acid) for 5 min. Chambers were washed with water. The levels of invasion were assessed by counting the number of cells present in 10 fields on the lower surface of the membrane, under light microscope (20).

(71) Reporter Assays and Constructs

(72) The miR-15a/miR-16 target genes UTRs were cloned in the Xba I site of pGL3 promoter, immediately downstream from the stop codon of the luciferase coding sequence. For Bcl-2, a 3UTR of 1329 bp fragment was amplified, corresponding to residues 2446-3774 of Genbank Acc No M14745. For cyclin D1 3UTR, a 1036 bp fragment was amplified (residues 3011-4078 of No NM_053056). For Wnt3a 3UTR, a 906 bp fragment was amplified (residues 2026-2932 of No NM_033131.2). For 3UTR cyclin D1 and Wnt3a mutagenesis, a five nucleotide mutation was inserted in the seed sequences interacting with miR-15a and miR-16 (see FIGS. 13A-C). Modified and HPLC purified oligonucleotides (Invitrogen) were used for amplification and mutagenesis, performed with Pfu enzyme following the in vitro mutagenesis kit protocol (Invitrogen). Transfection efficiencies of luciferase assays were normalized by calculating the ratio firefly/renilla. For each construct the relative luciferase activities were obtained by dividing the values obtained in the transfection of miR-15a and miR-16 by those of the non targeting miR scrambled. Each experiment was performed in duplicate and replicated five times.

(73) In Situ Hybridization

(74) Two m-thin sections were cut at the microtome, mounted onto poli-lysine-coated glass slides and processed for the hybridization. Briefly, slides were deparaffinized in xylene and hydrated by consecutive dipping in serial dilution of ethanol (100%, 75%, 50%, 25%). Sections were then treated for 5 min with 0.2N HCl, washed in phosphate-buffered saline (PBS, pH 7.4), digested with 40 g/ml of proteinase K for 25 min at 37 C., and post-fixed for 10 minutes with 10% formaldehyde in PBS. Following fixation, sections were acetylated for 10 min in acetic anhydride/triethanolamine (0.25% v/v acetic anhydride/0.1 M triethanolamine, pH8). Slides were then prehybridized in an oven at 50 C. for 2 hrs in hybridization buffer (65% formamide, 0.075 M sodium citrate (5SSC), 0.1% Tween-20, adjusted to pH 6.0 with 9.2 mM citric acid, 50 g/ml heparin, 100 g/ml yeast tRNA).

(75) Thereafter, slides were hybridized in incubation chambers overnight at 50 C. using 1 l from a 25 M stock of probe in 1000 l of prewarmed hybridization buffer. The day after, sections were washed twice in 5SSC, followed by 3 washes of 20 min at 50 C. in 50% formamide/2SSC. Slides were then rinsed 5 times in TBS/0.1% Tween-20 (TBST), and blocked for 1 hr in 4% BSA/TBST. A monoclonal anti-biotin antibody (Vector, U.K.) was applied on sections for 16 hrs at 4 C. After washing, sections were incubated for 1 hr with an alkaline phosphatase-conjugated anti-mouse IgG (Jackson Laboratories, Maine, USA). After secondary incubation, sections were washed twice 10 min each in staining buffer (100 mM Tris, 50 mM MgCl.sub.2, 100 mM NaCl, pH 9.5), followed by NBT/BCIP developing solution (Dako Cytomation, CA, USA) for 30 min at RT. After color development, slides were rinsed in TBS, ddH.sub.2O and were dehydrated by passing through a series of alcohols (50%, 75%, 95%, 100%) and xylene and coverslipped in PermaMount.

(76) In Vivo Assay

(77) Six-eight weeks old male NOD-SCID mice (Charles River Laboratory, Wilmington, Mass.) were used for examining the tumorigenicity of RWPE-1 decoy15/16 and RWPE-2 decoy15/16 cells, and for evaluation of cytotoxic activity of miR-15/miR-16 in LNCaP xenografts. A total of 200 l of cell suspension in Matrigel (1:1, vol/vol) was subcutaneously injected into the dorsal surface of mice. The number of cells injected was 410.sup.6 or 10.sup.7 for RWPE-1, 410.sup.6 for RWPE-2, and 810.sup.6 for LNCaP cells. Tumor incidence three weeks after subcutaneous injection in NOD-SCID mice of 810.sup.6 LNCaP cells in Matrigel was 90%.

(78) Six week old male BALB/c mice received a single dose of mixed antagomirs selective for miR-15 and 16 by intraprostatic injection through a transverse incision in the lower abdomen. Saline buffer and the unrelated cardio-specific antagomir targeting miR-1 were used as controls. Abdominal wall muscles were incised, and the bladder and seminal vesicles were delivered through the incision to expose the prostate. Antagomirs were injected via a 0.3 mm needle directly into the anterior prostate. The incision was closed using a running suture of 4-0 silk. Antagomirs were administered at the final dose of 80 mg/Kg of body weight in 0.2 ml per injection. Mice were not treated with testosterone during the experiments and were sacrificed after 5 weeks post injection.

Results

(79) miR-15a/miR-16 Expression in Prostate Tissues

(80) We first examined whether the low expression of the miR-15a/miR-16-1 cluster observed in chronic lymphocytic leukemia was a feature shared by prostate cancer. Therefore, we analyzed miR-15a and miR-16 expression in 20 patients with stage II-Ill prostate cancer. Freshly isolated surgical tumor specimens were collected and cultivated in a medium that allowed the propagation of prostate primary cells (see Supplementary Methods and FIGS. 7A-B). Non-tumoral samples from the same patients were used as a control reference.

(81) Real-time PCR showed a consistent downregulation of both miR-15a and miR-16 in about 80% of the tumor samples analyzed with respect to their normal counterparts, particularly in more advanced tumors (FIG. 1A and Table 1). To confirm that such a low expression in primary cultures mirrored the miR levels of prostate tumors, tissue sections prepared from 15 additional cases were examined by in situ hybridization with miR-15a and miR-16 probes. In 12 (miR-15a) and 13 (miR-16) of the 15 patients analyzed, these miRs were absent or weakly expressed in cancer epithelial cells, while their normal counterpart displayed a marked staining for both miRs (FIGS. 1B, 1C and FIG. 8).

(82) Scoring was performed using a semiquantitative system. The staining intensity for both normal and tumor cells included 4 scores: no staining (score 0), weak staining (score 1), moderately positive (score 2), and strongly positive (score 3). In the vast majority (9/15 for miR-15a and 8/15 for miR-16) of cases, tumor cells were completely negative (score 0) or displayed a weak staining (3/15 for miR-15a and 5/15 for miR-16; score 1) while the remaining (3 for miR-15a and 2 for miR-16) cases showed a moderate staining (score 2) of tumor cells. Both basal and luminal non neoplastic cells showed diffuse and constant miR expression, ranging from moderately (12/15 for miR-15a and 9/15 for miR-16) to strongly positive (3/15 for miR-15a and 6/15 for miR-16). Overall, the majority of the tumor samples analyzed showed an overt decrease in the level of both miRs as compared to the normal tissue, one of the prerequisites for the definition of classical tumor suppressor genes.

(83) Stable Expression of a miR-15a/miR-16 Decoy in RWPE-1 Recapitulates the Tumor Phenotype

(84) In order to explore the role of miR downregulation in the molecular mechanisms that regulate prostate cancer, we investigated the involvement of miR-15a/miR-16 loss in the course of tumorigenesis and exploited a depletion strategy in the untransformed and growth factor dependent prostate cell line RWPE-1, immortalized with human papilloma virus 18 [18]. For this purpose, we engineered a lentiviral vector named TW3UTR (TW3), in which we inserted multiple antisense sequences for miRs silencing to create a TW3UTR decoy miR-15a/miR-16 vector (decoy15/16) (FIG. 2A). This vector produces a stable EGFP transgene with multiple matching sequences for both miRs into 3 untranslated region (3UTR). The vector also includes a puromycin resistance cassette to selectively isolate transduced cells.

(85) Decoy transcript silencing was validated by Northern blotting and flow cytometry analysis, which showed a specific fluorescence reduction consistent with miR-15a/miR-16 binding to the EGFP 3UTR (FIG. 9A, FIG. 9B). Along with diminished EGFP-derived fluorescence (FIG. 10A), we observed a significant decrease of both miRs in decoy15/16 infected RWPE-1 cells (FIG. 2B and FIG. 10B), whose levels became slightly higher than those detected in 13q14-deleted LNCaP prostate cancer cell line[19]. A similar decrease in miR-15a/miR-16 expression was observed in primary prostate tumor cells expressing normal levels of both miRs (FIG. 2B).

(86) We next analyzed the growth kinetics of prostate cells upon loss of miR-15a/miR-16. RWPE-1 cells infected with decoy15/16 (RWPE-1decoy15/16) showed a considerable increase in the growth rate as compared to control cells infected with empty vector TW3UTR (RWPE-1TW3) (FIG. 2C). Likewise, downregulation of miR-15a/miR-16 in primary prostate tumor cells resulted in enhanced growth and considerably prolonged survival in culture as compared with control cells (FIG. 2C and data not shown). Such accelerated growth correlated with a significant increase in the percentage of cells at the S/G2-M phases of the cell cycle (FIG. 2D), indicating that targeting of miR-15a and miR-16 is able to enhance prostate cell proliferation. Thus, there is a causal relationship between miR-15a/miR-16 loss of expression and deregulated growth in untransformed prostate cells.

(87) Anchorage-independent growth is regarded as an in vitro surrogate to determine the tumorigenic capacities of transformed cells. We analyzed the effect of miR-15a/miR-16 depletion on the ability of RWPE-1 cells to form colonies in soft-agar. Differently from wild-type and control vector-transduced cells, RWPE-1 decoy15/16 cells were able to grow and give rise to colonies that exhibited anchorage independent growth (FIG. 2E). To investigate the possible effect of miR-15a/miR-16 downregulation on prostate cell migration, we performed a motility assay with RWPE-1decoy15/16 and RWPE-1TW3 cell lines on Boyden chambers containing porous polycarbonate membranes and maintained in two different conditions, either in conventional or in cancer fibroblast-conditioned medium. Unlike control cells, RWPE-1decoy15/16 cells revealed intrinsic migration capacity in standard medium, and enhanced invasion and motility in cancer fibroblast-conditioned medium (FIG. 2F). These data established a direct correlation between miRs silencing, increased proliferation and migration.

(88) Reconstitution of miR-15a and miR-16 Expression Induces Growth Arrest and Apoptosis in Prostate Tumor Cells

(89) To determine the consequence of miR-15a/miR-16 restoration in prostate cancer cells, the miR-15a/miR-16-1 cluster was amplified by PCR from human genomic DNA and subcloned into the TWEEN[20] lentiviral vector (TWmiR-15a/miR-16) (FIG. 3A). Then miR-defective LNCaP cells were transduced with this vector to obtain a near-physiological expression of miR-15a and miR-16, as evaluated by real time PCR (FIG. 3B). The RWPE-1 cell line was infected in parallel as a control reference to check for possible toxicity deriving from miR-15a/miR-16 overexpression. miR transduced LNCaP cells underwent growth arrest and apoptosis, while RWPE-1 did not show any sign of toxicity (FIGS. 3C, 3D). After gene transfer, the few surviving TWmiR-15a/miR-16 LNCaP cells underwent massive counterselection that was not observed in LNCaP cells transduced with control vector or in TWmiR-15a/miR-16 RWPE-1 cells (FIG. 3E), suggesting that loss of miR-15a/miR-16 creates addiction in transformed cells.

(90) The tumor suppressor Rb is located 1.7 Mb upstream of miR-15/16 in the 13q14 region [11] [21]. To rule out that the absence of Rb may contribute to the tumor phenotype of 13q14 deleted LNCaP cells, we investigated Rb expression in LNCaP cells lacking miR-15/16. Western blotting analysis showed that miR-defective LNCaP cells did not lose the expression of Rb (FIG. 11A), indicating that they represent a useful system to study the involvement of miR-15/16 deletion in prostate cancer progression. Moreover, the analysis of primary prostate cells did not show a significant correlation between Rb and miR-15/16 levels (FIG. 11B), suggesting that the loss of miR-15/16 is often independent of the absence of Rb.

(91) Docetaxel is the standard treatment for androgen-independent prostate tumors [2]. The ability of miR-15a and miR-16 to target Bcl-2 may influence the pharmacological response of prostate cells. Hence, we reasoned that abrogation of this regulatory circuit through loss of miR-15a/miR-16 expression in prostate cancer might enhance chemoresistance and reduce the efficacy of medical treatments. To validate our hypothesis, we analyzed the chemosensitivity of RWPE-1 cells transduced with decoy15/16 cells. Upon targeting of miR-15a/miR-16, RWPE-1 became more resistant to docetaxel treatment and behaved similarly to miR-15a/miR-16-defective LNCaP cells, both in terms of caspase activation and cytotoxic response (FIG. 12A, 12B). In order to determine the possible additive effect of miRs and chemotherapy, we evaluated the cytotoxic activity of docetaxel on miR-15a/miR-16 reconstituted LNCaP cells.

(92) miR-15a/miR-16 expressing prostate cancer cells were massively killed by docetaxel exposure, while the empty vector-transduced population was scarcely sensitive (FIG. 12B). To confirm the data obtained in cell lines, we performed similar experiments on primary cells from miR-defective primary tumors. Purified primary prostate cells from tumoral and control tissues were transduced with TWmiR-15a/miR-16 or TW empty vector. Transgenic miR expression was evaluated by real time PCR (FIG. 3F). Restoration of miR-15a/miR-16 expression dramatically impacted on the viability of primary prostate tumor cells, while normal cells did not suffer from toxicity upon miR overexpression (FIG. 3G). These data suggest a miR-elicited pro-apoptotic effect in tumoral cells that might be exploited to sensitize cells to chemotherapeutic regimens.

(93) To verify this possibility, prostate primary cells transduced with miR-15a/miR-16 were treated with docetaxel. As for LNCaP cells, the combination of miRs and chemotherapy was dramatically effective in killing miR-15a/16 defective primary prostate cancer cells (FIG. 12C). In contrast, early stage primary prostate cancer cells expressing miR-15a/16 acquired resistance to docetaxel upon targeting of miR-15a/16 (FIG. 12C), indicating a clear dependence on miR-15a/miR-16 expression for chemosensitization. Thus, reconstitution of miR-15a/miR-16 in defective prostate cancer cells induces a considerable cytotoxic activity that is further increased by the combined use of chemotherapy.

(94) miR-15a/miR-16 Target the Cyclin D1 and Wnt3a 3UTR

(95) miR-15 and miR-16 can directly target Bcl-2 mRNA and thus induce apoptosis in chronic lymphocytic leukemia cells[16]. However, based on the increased proliferation and invasiveness observed in untransformed prostate cells depleted of miR-15a and miR-16, we speculated that additional targets of these miRs could be involved in such a malignant phenotype. Therefore, we ran a computer-assisted search that generated a list of >400 potential targets, which we refined by applying increasing stringency in the selection criteria (see Methods). Among the possible candidates, we analyzed further cyclin D1, Wnt3a and Pim-1, three genes whose functions were directly associated with cancer progression and invasion [22-24].

(96) Cyclin D1 and Wnt3a showed a particularly high prediction ranking, while Pim-1 displayed a higher estimated false discovery rate (Table 2). To validate our targets, we subcloned the 3UTR of these genes at the 3 of the cDNA encoding luciferase in an expression construct and performed cotransfection experiments with miR-15a/miR-16. We narrowed our analysis to 1 kb regions harbouring the putative miR-15a/miR-16 target sites. The Bcl-2 3UTR was tested in parallel as positive control. Luciferase assay was performed by cotransfecting pGL3-3UTR vectors along with synthetic miR-15a, miR-16 and a control miR with a scrambled sequence.

(97) We observed a consistent reduction in reporter activity only when positive control and putative target vectors were assayed in combination with either miR-15a or miR-16, but not with scrambled oligos (FIG. 4A). The luciferase activity decrement indicated a direct interaction of both miR-15a and miR-16 with cyclin D1 and Wnt3a 3UTRs to the same extent as measured for Bcl-2, while Pim-1 UTR could be confirmed as a non-targeted region (FIG. 4A and FIG. 13A). As an endeavour to refine the identification of regulatory sites, we mutated the seed sequence of the putative target sites in the cyclin D1 and Wnt3a 3UTRs (FIG. 13B).

(98) 3UTR mutations rendered the constructs immune to regulation by miR-15a/miR-16, evidencing the specific binding of both miRs to the cyclin D1 and Wnt3a mRNAs (FIG. 13C).

(99) To further validate our findings, we evaluated the variation in the target gene proteins upon modulation of miR-15a/miR-16. Protein lysates were prepared from cells transduced so as to increase (TWmiR-15a/miR-16) or decrease (decoy15/16) the levels of miR-15a/miR-16 with respect to a control (TW or TW3). For the depletion experiments, we examined the levels of target proteins in RWPE-1 cells and their transformed derivative RWPE-2. Western blot analysis consolidated the data obtained with the reporter gene assays for Bcl-2, Wnt3a and cyclin D1, showing a significant increase in their protein levels upon expression of the decoy15/16 (FIG. 4B, FIG. 14A). These data were also confirmed in a complementary approach using TWmiR-15a/miR-16 to increase the levels of miR-15a and miR-16 in LNCaP and miR defective primary tumor cells, resulting in a sensible decrease of all the three proteins (FIG. 4B, FIGS. 14B, 14C).

(100) To consolidate the data obtained with lentiviral vectors, sense and antisense oligos specific for miR-15 and miR-16 were delivered into wild type RWPE-1 cells. As expected, miR-15 and 16 oligos reduced the expression of Bcl-2, cyclin D1 and Wnt3a, while cells treated with antisense oligos showed a target protein up-regulation comparable to RWPE-1Decoy15/16 cells (FIG. 4C), which was reverted following transfection with miR-15 and 16 oligos (FIG. 4C). We next analyzed miR-15a/miR-16 defective prostate tumors for expression of Bcl-2, cyclin D1 and Wnt3a. The availability of reliable reagents for two of the three targets allowed the immunohistochemical analysis of Bcl-2 and cyclin D1, which were found upregulated in miR-15a/miR-16 defective prostate tumors (FIG. 4D). Moreover, the immunoblot analysis of primary prostate cultures indicated a significant inverse correlation (P=0.008) between miR-15/16 expression and target protein levels (FIG. 4E).

(101) Wnt3a signalling promotes the increase in -catenin protein levels and the activation of other survival and proliferation pathways through the phosphorylation of ERK and Akt [25, 26]. Accordingly, the analysis of TWmiR-15a/miR-16 LNCaP and RWPE-1decoy15/16 cells showed that the presence of miR-15a and miR-16 was associated with a decreased expression of -catenin and a reduced phosphorylation of AKT and ERK (FIG. 4F and FIG. 14D). Moreover, the increased expression of cyclin D1 in RWPE-1decoy15/16 cells correlated with an increased phosphorylation of Rb, whereas the exogenous expression of miR15/16 in LNCaP cells produced an opposite effect (FIG. 4F and FIG. 14D).

(102) Thus, miR-15a and miR-16 act by targeting the mRNAs of Bcl-2, cyclin D1 and Wnt3a, which promote prostate cell survival, proliferation and invasion.

(103) In order to clarify the role of the single target genes in prostate cancer progression, we infected RWPE-1 cells with virus particles containing transgenes for Bcl-2, cyclin D1 and Wnt3a. Both cyclin D1 and Wnt3a upregulation considerably increased prostate cell growth and the percentage of cells at the S/G2-M phase of the cell cycle, while exogenous expression of Bcl-2 did not alter significantly cell growth or cell cycle profile (FIGS. 15A, 15B). The in vitro migration analysis revealed that Wnt3a promotes the invasion and motility of RWPE-1 cells, which was not affected by exogenous expression of Bcl-2 or cyclin D1 (FIG. 15C), suggesting that the increase expression Wnt3a and cyclin D1 mediate the accelerated growth after miR-15a and miR-16 downregulation, while Wnt3a upregulation is responsible for the enhanced migration.

(104) To investigate the contribution of the three targets of miR-15a and miR-16 in docetaxel resistance, Bcl-2, cyclin D1 and Wnt3a transduced RWPE-1 cells were treated with the chemotherapeutic drug. After single gene transduction, only Bcl-2 cells was able to protect prostate cells from docetaxel (FIGS. 16A, 16B). Moreover, the concomitant upregulation of Bcl-2 and Wnt3a synergistically counteract the cytotoxic activity of docetaxel (FIGS. 16A, 16B), suggesting that both targets mediated the enhanced survival that follows the loss of miR-15a and miR-16.

(105) Targeting of miR-15a/miR-16 Promotes Tumorigenesis and Tumor Progression

(106) To further elucidate the significance of miR-15a/miR-16 loss as a critical step in cancer development and progression, NOD-SCID mice were used as an in vivo model for prostate cancer xenografts. Since miR silencing proved sufficient to enhance the proliferation of RWPE-1 cells and conferred a growth and migratory behaviour reminiscent of neoplasms, we investigated whether the loss of function of miR-15a and miR-16 would endow the non-tumorigenic cell line RWPE-1 with the ability to form tumors in NOD-SCID mice. RWPE-1 transduced with either decoy15/16 or empty vector were injected subcutaneously into 4 week old male mice. RWPE-1 decoy15/16 were able to consistently produce slow growing tumors, whereas RWPE-1 TW3 did never develop into a tumoral mass (FIG. 5A).

(107) To determine the possible synergism with other oncogenic lesions, we devised a similar experiment with the RWPE-2 cell line transduced with decoy15/16 vector. RWPE-2 cells are able to produce small tumors in vivo, as they have been transformed by insertion of the ki-RAS gene into RWPE-1 cells [18]. RWPE-2 cells have the same levels of miR-15a and miR-16 expression of RWPE-1 cells, as revealed by real time PCR (data not shown). When injected into NOD-SCID mice, RWPE-2decoy15/16 produced tumors with a significantly increased volume as compared with TW3 transduced cells (FIG. 5B). We next injected subcutaneously in NOD-SCID mice a combination of wild type (70%) and decoy15/16-transduced (30%) RWPE-1 cells. After tumor formation, we analyzed by immunohistochemistry the localization of decoy15/16-transduced cells through the staining of the GFP reporter. Such analysis revealed that miR-15a/miR-16 downregulation enhances prostate cell invasion, as indicated by the presence of GFP+ cells in the tumor front and in invasive tumor islands (FIG. 5C). Hence, miR-15a/miR-16 downregulation can contribute to prostate cancer transformation, suggesting a causative role in tumor progression.

(108) Antagomir oligonucleotides can efficiently knockdown specific miRNAs in most tissue in vivo for as long as 1 month after injection [5, 27]. To investigate the role of miR-15a/miR-16 downregulation in prostate in vivo, we injected into BALB/c mouse prostate a single dose of mixed antagomirs selective for miR-15a and 16. As controls, mice were injected with either saline buffer or antagomir selective for the unrelated cardio-specific miR-1. Inhibition by antagomir was evaluated using Real time PCR assay from one week to one month post injection, resulting in 40-85% repression of endogenous miR-15a and 16 over antagomir-1 treated mice (data not shown). Five weeks after antagomir injection, histological analysis showed a marked prostatic hyperplasia and a modest acini disruption in antagomir-15/16 treated mice, while control mice did not show any alteration (FIG. 5D), in line with the potential tumor suppressor role played by the cluster miR-15a/miR-16.

(109) Therapeutic Effect of miR-15a/miR-16 Reconstitution on Prostate Tumor Xenografts

(110) The tumor suppressor activity of the cluster miR-15a/miR-16 seems required for the homeostatic regulation of the prostate epithelial tissue. Our in vitro experiments showed that miR-15a/miR-16 reconstitution in defective prostate cells resulted in growth arrest and apoptosis. To evaluate the effect of restored miR-15a/miR-16 expression in an in vivo tumoral model, 810.sup.6 LNCaP cells resuspended in Matrigel were injected subcutaneously in NOD-SCID mice. This procedure gave rise to the formation of tumors within 2-3 weeks (FIG. 6A). Four weeks postinjection, tumor xenografts were locally treated with TWmiR-15a/miR-16 or TW control viruses in order to obtain the transduction of the vast majority of the cancer cells resident into the tumor mass (FIG. 6B). TWmiR-15a/miR-16 injected tumors underwent growth arrest within one week from treatment, while similar tumors did not alter their growth after injection with empty-vector virus. Moreover, 2 weeks after virus treatment, we observed a considerable volume regression of TWmiR-15a/miR-16 infected tumors, while control tumors continued to grow exponentially (FIG. 6A). The anti-tumor effect of miR-15a/miR-16 treatment was particularly potent and not confined to tumor reduction, as the histological analysis of the residual masses indicated the presence of diffuse necrosis with rare areas containing surviving cells (FIG. 6C). Thus, in line with the in vitro observations, restoration of miR-15a and miR-16 in defective prostate cancer cells resulted in dramatic tumor regression.

Discussion

(111) Advanced prostate cancer is a severe condition frequently leading to patients' death [1]. The identification of the mechanisms responsible for tumor initiation and progression may contribute significantly to devise more effective therapeutic strategies. Here, we demonstrated that miR-15a and miR-16 are downregulated in a considerable percentage of prostate tumors, particularly in advanced stages. In vitro and in vivo targeting of miR-15a and miR-16 enhances prostate cell survival while promoting cell growth and invasion. Both miRs are able to target Bcl-2, cyclin D1 and Wnt3a, whose protein levels are consequently upregulated when the miRs are downregulated and may contribute to potentiate tumor cell survival, proliferation and invasion.

(112) Bcl-2 protein is barely detectable in normal human prostatic secretory epithelial cells, whereas high levels of this pro-survival oncoprotein are found in neoplastic prostate tissues, particularly in hormone-independent prostatic adenocarcinomas[28-30]. Accumulating evidence indicates the involvement of Bcl-2 in human prostate cancer development [31]. Increased Bcl-2 expression promotes the resistance to chemotherapy[17] and androgen depletion[28]. Thus, Bcl-2 upregulation in miR-15a/miR-16 defective prostate cancer may contribute to tumor progression and resistance to therapy.

(113) Cyclin D1 is an essential regulator of cell cycle progression that interacts with cyclin-dependent kinase (CDK) 4/6 to form an active kinase complex that phosphorylates the retinoblastoma tumor suppressor, enabling the cell to undergo the G1/S phase transition of the cell cycle. About 40-50% of primary carcinoma overexpress cyclin D1, which is clearly implicated in the unrestrained proliferation observed in many tumors [22, 32]. The expression of cyclin D1 significantly predicted cancer-related survival and was associated with the Ki67 proliferative index in prostate cancer patients [22, 33]. Moreover, cyclin D1 expression correlated with prostate tumor grading and staging [33, 34], suggesting that its overexpression may represent a critical oncogenic event for cancer spreading.

(114) Several lines of evidence indicate a possible role of Wnt signalling in the oncogenic process leading to prostate cancer [23, 35]. The activation of the Wnt pathway results in inhibition of -catenin phosphorylation by GSK3, with consequent -catenin accumulation and transcription of a variety of cancer associated genes [23, 36]. In addition, Wnt3a promotes the activation of ERK and AKT with consequent phosphorylation of downstream substrates implicated in cell survival and proliferation [25, 26]. A recent study demonstrated a central roles for AKT and ERK signalling pathways in promoting prostate tumor progression to hormone-refractory state [37]. Moreover, a unique role for the Wnt3a growth factor in inducing androgen receptor-mediated transcription and cell growth in prostate cancer has been demonstrated, suggesting that its aberrant expression may play a critical role in prostate tumor progression[38].

(115) The ability of miR-15a/miR-16 to target Wnt3a may have considerable implications in prostate cancer. Upon Wnt3a upregulation, miR-defective tumors accumulate -catenin and activate a series of signalling events involved in cancer development and progression, such as the AKT and ERK pathways. Hence, it is reasonable to assume that loss of miR-15a/miR-16 during prostate carcinogenesis might represent an important oncogenic step mediated by Bcl-2, cyclin D1 and Wnt3a overexpression. Higher levels of Bcl-2 and Wnt3a may increase prostate cell growth by inhibiting apoptosis in unfavourable conditions, as in case of anti-androgen or cytotoxic therapies. Both cyclin D1 and Wnt3a are able to promote the proliferation of prostate cells upon silencing of miR-15a and miR-16, while the single increase in Wnt3a expression seems responsible for the enhanced migration and invasiveness typical of the advanced stages. Although it is theoretically possible that other targets may be involved in the oncogenic activities promoted by the loss of miR-15/miR-16, Bcl-2, cyclin D1 and Wnt3a play a key role in prostate cancer progression and represent the most likely target candidates for the tumor suppressor activity of this miR cluster.

(116) The data presented here has considerable therapeutic significance for advanced prostate cancer. Clinical trials aimed at assessing the therapeutic potential of antisense oligodeoxynucleotides targeting Bcl-2 gene expression in prostate cancer have been undertaken [39]. The reintroduction of miR-15a/miR-16 could be theoretically more effective due to the simultaneous targeting of Bcl-2, cyclin D1 and Wnt3a, three major proteins involved in resistance to apoptosis and cancer cell proliferation.

(117) In our experimental models, delivery of miR-15a and miR-16 in prostate cancer xenografts was able to induce a dramatic tumor regression. The cytotoxic effect of these miRs on both LNCaP and primary prostate tumor cells was striking, and further increased in the presence of docetaxel. Thus, although advanced prostate tumors are extremely heterogeneous in the clinical setting, it is likely that miR-15a and miR-16 can have a considerable therapeutic potential, both as single agents or in combination with chemotherapeutic drugs.

(118) Advanced molecular therapies aimed at downmodulating the level of a given miR in model organisms have been successfully established [5, 27], while siRNA-based strategies for the introduction of artificial RNA guide strands in the RNA-induced signalling complex (RISC) proved their efficacy in primates[40]. We thus envision that the aim of restoring miR-15a/miR-16 function for prostate cancer therapy might take advantage of a siRNA mimicker, whereby the guide strand of these miRs might be embedded in a synthetic sequence or in its native pre-miR sequence context.

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EXAMPLE 2

(120) BTG2 is a prototype member of the BTG/Tob family of antiproliferative proteins, initially identified as early growth response genes induced by growth factors and tumor promoters. BTG2 has subsequently been characterized as a pan-cell cycle modulator and a major effector of p53-induced proliferation arrest due to its ability to inhibit the expression of cyclin D1 and the phosphorylation of Rb (Boiko A D 2006). Repression of BTG2 cooperates with Ras activation in inducing cell transformation, indicating BTG2 as a tumor suppressor gene. BTG2 may also be involved in the direct induction of apoptosis in tumor cells, as its mouse ortholog TIS21 participates to mitochondrial depolarization and cell death by binding to the prolyl isomerase Pin1 (Hong J W 2005). BTG2 has lately been demonstrated to enhance chemotherapy-induced death of cancer cells by controlling the generation of oxidation products (Lim, Y B 2008 and Example 2, Refs-1-8).

(121) MicroRNA-21 (miR-21) has been found to be upregulated in microarray studies involving breast, colon, lung, pancreas, prostate and stomach tumors (Volinia et al., 2006). MiR-21 knockdown induces apoptosis in glioblastoma cells (Chan et al., 2005) and sensitizes cholangiocytes to chemotherapeutic agents (Meng et al., 2007), while its overexpression inhibits apoptosis in myeloma cells (Loffler et al., 2007). MiR-21 has been shown to target and down-regulate the expression of the tumor suppressors tropomyosin 1 (Zhu et al., 2007), phosphatase and tensin homolog (PTEN) (Meng et al., 2007), and programmed cell death 4 (PDCD4) and to promote cell invasion and metastasis (Asangani et al., 2007). Moreover, interfering with miR-21 activity inhibits tumor growth in vivo and in vitro (Si et al., 2007), demonstrating the importance of this gene in regulating tumorigenesis.

(122) We have shown that miR-21 expression is elevated in prostate cancer and identified BTG2 as a target of miR-21. We have shown that miR-21 overexpression reduces BTG2 levels and increases the growth of prostate cancer cells. In particular, we show that infection of prostate cancer cells with a lentiviral vector that specifically abrogates the action of miR-21 on BTG2 transcripts results in increased BTG2 expression and inhibits the growth of tumor cells in vitro and in vivo. The use of such vectors allowed to demonstrate that the deregulated expression of miR-21 contributes to the expansion of prostate tumors through the specific silencing of BTG2.

(123) Elevated BTG2 Expression Decreases Prostate Cancer Cell Tumorigenicity.

(124) Exogenous expression of BTG2 in prostate cancer cell lines results in decreased rates of cell proliferation (FIGS. 17A-G and 18A-D). We sought to investigate the role of miR-21-mediated BTG2 modulation by producing a model system in which the expression of BTG2 was regulated in an endogenous fashion by specifically interfering with miR-21 action on BTG2 3UTR.

(125) Therefore, we engineered a lentiviral vector in which we inserted the 3UTR of BTG2, the miR-21 binding sites in the 3UTR of EGFP (Enhanced Green Fluorescent Protein) and a puromycin resistance cassette to selectively isolate transduced cells (FIG. 17A). This vector was called TWEEN-3-UTR-BTG2 (TW3UTRBTG2) and was used to produce a stable EGFP transgene with a chimera 3UTR able to bind miR-21 and to control BTG2 transcription in RWPE-2 cells. Chimera transcript targeting was validated by flow cytometry analysis of BTG2 levels in RWPE-2 cells transduced with TW3UTRBTG2, which showed significantly increased BTG2 levels in EGFP-expressing cells.

(126) The effect of TW3UTRBTG2 on restoring endogenous levels of BTG2 was validated also on 22Rv1 prostate cancer cells. Elevated BTG2 expression resulted in decreased growth rates in TW3UTRBTG2-infected cells which was due mainly to a decrease of cells in the S phase of the cell cycle (FIGS. 17C, 17D). According to the decreased proliferative activity of TW3UTRBTG2-infected cells, we found significantly reduced levels of cyclin D1 and pRb, whereas the expression of PTEN, another known miR-21 target, remained unchanged (FIG. 17E). Levels of Cyclin D1 and pRb detected in TW3UTRBTG2-infected cells approximated those found in the non-transformed prostate cell line RWPE-1 (which differs from RWPE-2 for the presence of oncogenic Ras) (FIG. 17E), suggesting that miR-21-mediated BTG2 silencing provides an important contribution to cellular transformation.

(127) BTG2 Upregulation Impairs Tumor Growth Rate In Vivo.

(128) To investigate the influence of endogenous BTG2 modulation on tumor progression, we injected RWPE-2 cells subcutaneously into NOD-SCID mice and we treated the established prostate tumors with virus particles containing TW3 or TW3UTRBTG2 vectors. Tumor size was evaluated starting from the time of virus injection for 12 days. While vector-treated tumors showed a constant growth rate, TW3UTRBTG2-treated tumors showed a significant growth reduction starting from the time of virus injection (FIG. 19).

(129) In TW3UTRBTG2-treated tumors, we found increased BTG2 levels compared to controls and areas of apoptotic cells, as revealed by H&E or TUNEL staining. These results indicate that restoration of endogenous BTG2 expression using such vectors specifically blocks miR-21 targeting and results in decreased aggressiveness and increased apoptosis of tumor cells in vivo.

Material and Methods

(130) Cells and Antibodies.

(131) RWPE-1, RWPE-2, LNCaP, 22Rv1, CaHPV10, PC3 and DU145 cell lines were obtained from ATCC and cultivated in the recommended medium. Tissue dissociation and isolation of primary prostate cells were performed as described [43]. Normal and neoplastic prostate surgical specimens were cultured in collagen-coated plates with BRFF-HPC1 medium (AthenaES, Baltimore, Md.), where cells grew in monolayer assuming a round-shape aspect. To determine the number of luminal cells and contaminating fibroblasts in tumor specimens, cells were stained for cytokeratin 18 (Clone5D3, NovoCastra) and Thy-1 (Clone 5E10, Becton Dickinson) respectively. The percentage of tumor cells was evaluated with anti-AMACR (Sanova Pharma, Vienna, Austria), while normal basal cells were detected with anti-p63 (BioGenex). For flow cytometry, Thy-1 staining was performed in PBS at 4 C. for 1 h, while the other antibodies were used after fixation and permeabilization with 2% parafolmaldehyde and 0.1% Triton X-100. The purity of human prostate primary cell preparation was confirmed by immunocytochemistry and only cultures with >85% enrichment of prostatic epithelial cells were used for subsequent experiments. Tissues were obtained from radical prostatectomy at the Department of Urology, S. Giovanni Bosco Hospital, Turin, Italy. All samples were collected with the informed consent of the patients. Antibodies against BTG2 were obtained as in Example 2, Ref.6 (Farioli-Vecchioli S. FASEB J. 2007 July; 21(9):2215-25. Epub 2007 Mar. 19).

(132) Generation of Lentiviral Vectors and Gene Transfer.

(133) For TWmiR-21 generation (TWmiR-21), miR-21 precursor DNA was PCR-amplified from human genomic DNA. The amplified fragment spanning 724 bp (MI0000077 genome context Coordinates (NCBI36 17: 55273409-55273480 [+]) was subcloned into the lentiviral vector TWEEN [22] under the CMV promoter. miRNA transgene expression was assayed by real time PCR using the appropriate oligonucleotides from Applied Biosystems. The TW3UTR vector was obtained by modifying the EGFP 3UTR of the TWEEN vector through the insertion of a multicloning site (XhoI-XbaI) that allowed the subcloning of the sequences of interest. Then the EGFP modified 3UTR cassette was inserted under the CMV promoter control.

(134) Moreover, a puromycin resistance gene was inserted under the PGK promoter control to allow the selection of transduced cells. To generate the TW3UTRBTG2 vector, about 400 bp of 3BTG-2UTR, containing miR-21 binding site, was subcloned into XhoI-XbaI multicloning site in TW3UTR vector. This design was intended to optimize repression of the transgene in the presence of the miR21 and simultaneously derepression of endogenous BTG-2 mRNA. In fact from TW3UTRBTG2 vector is generated an artificial transcript composed of EGFP with a 3modified UTR containing a fragment of BTG-2 3UTRs The sequestering/derepressing capacity of this vector was validated as reported in FIGS. 4A-F. In this figure all the experiments report derepression of BTG-2 protein translation underlying no activity on other miR-21 target genes such as PTEN. (FIG. 17E). Recombinant lentiviral particles were obtained as described [46] by infecting cells with 110.sup.6 (TU)/ml viral particles. For in vivo experiments, the viral supernatant was concentrated 250-fold by ultracentrifugation and injected directly into tumor xenografts of NOD-SCID mice.

(135) Reporter Assays.

(136) 3UTR segments of BTG2 was amplified by PCR from normal human genomic DNA and subcloned into the 3UTR of the firefly luciferase coding sequence into pGL3-Promoter (Promega). Then K562 (510.sup.4 cells per well) were transfected using Lipofectamine 2000 (Invitrogen) following the manufacturer's instructions. Transfection mix included: (a) 0.8 g of pGL3-3UTR plasmid and 50 ng of the control vector pRL-TK (Promega); (b) 25 pmol of either non-targeting RNA control (scrambled) or miR-21 oligonucleotide (Ambion). Forty-eight hours post-transfection, firefly and renilla luciferase activities were measured using the Dual Luciferase Assay kit (Promega). Transfection efficiencies were normalized by calculating the ratio firefly/renilla. For each construct the relative luciferase activities were calculated by dividing the values obtained in the transfection of miR-21 by those of miR scrambled. Each experiment was performed in duplicate and replicated five times.

(137) Flow Cytometry and Viability Assays.

(138) For cell cycle determination, 2.510.sup.5 RWPE-2TW3 and RWPE-2BTG2-3UTR cells were analyzed with the BD Pharmingen BrdU Flow Kit staining protocol. Cells were seeded in 6 wells plate for 24 h. Then BrdU was added in culture medium and maintained for 1 h at 37 C. in incubator. Fixation and permeabilization of the cells was performed with BD Cytofix/Cytoperm Buffer following the protocol indication. Cells were stained with anti-BrdU-APC for 20 minutes at room temperature and treated with 7-AAD before FACS analysis. BrdU-unlabelled cells from the same population were used as negative control. Cells were analyzed with LSR II (BD). Cell growth and death was evaluated by trypan blue staining, Apo-percentage assay (Biocolor) and Cell Titer kit (Promega).

(139) Statistical analysis. Data are presented as the means.d. Results of BrdU assays were analyzed by two-way ANOVA and Bonferroni post-tests.

Discussion

(140) The functional consequence of miR-21 overexpression in prostate epithelial cells was an increase in proliferative ability which paralleled an inhibition of BTG2 expression. However, miR21 targets genes with apoptotic and regulatory functions such as PDCD4 and PTEN (Example 2, Ref 8-11) which could contribute to the phenotype of miR-21-overexpressing prostate cells. To define the role of miR-21-mediated BTG2 silencing we engineered a lentiviral vector, which acts as a decoy by specifically releasing miR-21 repression of BTG2 (i.e. de-repressing BTG2 expression). In this way, we could study the effect of restoring endogenous BTG2 expression rather than expressing exogenous BTG2 in prostate cells. This experimental system recapitulates more closely a situation in which BTG2 could be restored through the use of therapeutic tools and provides indications on the efficacy of such strategy in vivo. In fact, we found that cells in which BTG2 expression has been derepressed through the use of the UTR-BTG2 vector reverted to a less aggressive phenotype, as shown by reduced growth rates in vitro and decreased aggressiveness in vivo.

(141) BTG2 has been previously shown to exert its tumor suppressor activity by linking the p53 and the Rb pathways through a control circuit that is lost during neoplastic transformation (Boiko 2006). This mechanism seems to be implicated also in prostate tumorigenesis, as shown by the downregulation of cyclin D1 and pRb that resulted from BTG2 derepression. Interestingly, cyclin D1 and pRb levels in BTG2-derepressed prostate cancer cells returned more similar to those found in non-transformed prostate epithelial cells. Altogether, these observations suggest that BTG2 lies at a central point in the control of prostate tumorigenesis as it links Ras, p53 and Rb pathways resulting in final control of cell growth.

(142) Inhibition of miR-21 action on BTG2 in vivo by the UTR-BTG2 vector results in decrease of tumor aggressiveness, which is apparently due to the formation of apoptotic areas within the tumor mass. This observation is in accordance with recent observations by Lim et al. that BTG2 enhances the susceptibility of neoplastic cells to apoptosis, suggesting that the proapoptotic action of BTG2 may contribute to its role as a tumor suppressor.

(143) In conclusion, we have shown (for the first time) that miR-21 promotes prostate tumorigenesis by post-transcriptionally targeting BTG2 thus increasing prostate cell proliferation and survival. Use of the above described vector system reduced tumor growth in vivo by interfering with this regulatory loop (by specifically abrogating miR-21 action on BTG2 transcripts). These vectors, therefore allowed us to demonstrate that modulation of the miR-21/BTG2 axis may have therapeutic relevance for prostate cancer treatment. The use of this vector system is also widely applicable for other miRs and 3UTRs of genes to be investigated.

(144) The previously described decoy vectors repress the total amount of microRNA, whereas the 3UTR-mediated vectors sequester only some of the target microRNA and derepresses the protein of interest. The TW3UTR vector is similar to that described in Example 1.

(145) The TW3UTR vector was obtained by modifying the EGFP 3UTR of the TWEEN vector through the insertion of a multicloning site (XhoI-XbaI) that allowed the subcloning of the sequences of interest. Then the EGFP modified 3UTR cassette was inserted under the CMV promoter control. Moreover, a puromycin resistance gene was inserted under the PGK promoter control to allow the selection of transduced cells (as before). To generate the TW3UTRBTG2 vector, about 400 bp of 3BTG-2UTR, containing mir-21 binding site, was subcloned into XhoI-XbaI multicloning site in TW3UTR vector.

(146) This design was intended to optimize repression of the transgene in the presence of miR21 and simultaneously derepress endogenous BTG-2 mRNA. TW3UTRBTG2 vector generates an artificial transcript (chimera) composed of EGFP 3modified UTR containing a fragment of BTG-2 3UTR. The chimera transcripts quantitatively compete with endogenous BTG2 for mir-21 biding (and therefore repression). The repression of other genes repressed by mir21 is not significantly affected, see FIG. 17B, 17F, where derepression of BTG-2 protein translation was not shown in the other mir-21 target genes such as PTEN, p63 and sprouty2.

(147) BTG-2 upregulation can be detected by cytofluorimetric assays. Western blotting revealed signal cascade activation after BTG-2 overstimulation. BTG-2 induces inhibition of proliferation, Cyclin D1 repression, and a reduction in Rb phosphorylation.

(148) This kind of vector can be used to derepress only the gene of interest and not other targets of the same miRs. This is of great interest in the miRNA field because miRNAs have many targets and their function can vary with cell type. For the first time, we demonstrated that it is possible derepress only a target gene, maintaining the same levels for the others.

(149) Not all miRNA can be classified as tumor suppressors or oncomirs. More importantly, miRNAs can differentiate their role between tissues and pathologies. Since miRNA could have multiple targets, groups of then can be useful for tumor regression, but other subgroups may actually promote cancer progression.

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